Cherubism: Early Surgical Approach and Its Effects on the Quality of Life in a Pediatric Patient

Laryssa Thainá Mello Queiroz Cunha; Almira Oliveira Pereira; Roniery Correia Santos; Eduardo Zancopé; Sebastião  Alves Pinto; Valtuir Barbosa Félix; Rubens Jorge Silveira

doi:10.5327/2525-5711.326

Authors

Laryssa Thainá Mello Queiroz Cunha Department of oral diagnosis, Semiology and oral Pathology areas, Piracicaba Dental School, State University of Campinas (UNICAMP) https://orcid.org/0000-0003-1357-4129
Almira Oliveira Pereira Department of oral diagnosis, Semiology and oral Pathology areas, Piracicaba Dental School, State University of Campinas (UNICAMP)
Roniery Correia Santos Department of Psychology, IPOG - Instituto de Pós-Graduação e Graduação, Goiânia, Goiás, Brazil https://orcid.org/0000-0002-8481-1147
Eduardo Zancopé Department of Occlusion, Fixed Prosthesis and Dental Materials, School of Dentistry, Federal University of Uberlândia, Uberlândia, Minas Gerais, Brazil https://orcid.org/0000-0002-6567-4810
Sebastião Alves Pinto 5Pathologist, Goiano Institute of Oncology and Hematology, Goiânia, Goiás, Brazil
Valtuir Barbosa Félix Department of Oral Pathology, University Hospital of the Federal University of Alagoas, Maceió, Alagoas, Brasil https://orcid.org/0000-0002-2961-2487
Rubens Jorge Silveira Department of Oral and Maxillofacial Surgery and Traumatology, Pontifical Catholic University of Goiás (PUC - GOIÁS), https://orcid.org/0000-0002-3234-2158

DOI:

https://doi.org/10.5327/2525-5711.326

Keywords:

Cherubism, Facial deformities, Quality of life

Abstract

Cherubism is a rare fibro-osseous osteodysplasia characterized by the symmetrical expansion of the jaws, often leading to facial deformities and functional impairment. This study presents the case of a pediatric patient diagnosed with cherubism who underwent early surgical intervention to improve quality of life and reduce the psychosocial impacts associated with the disease. The PedsQL™ 4.0 questionnaire was applied to assess quality of life before and after the surgical procedure. The results demonstrated a significant improvement in the social and school domains, reflecting a reduction in the psychosocial burden of cherubism. Six months post-procedure, no significant complications or signs of recurrence were observed, highlighting the efficacy of early intervention. These findings suggest that an early surgical approach is a valuable strategy for optimizing quality of life and minimizing the negative effects of cherubism, particularly in children undergoing social and academic development.

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