Cherubism: Early Surgical Approach and Its Effects on the Quality of Life in a Pediatric Patient

Laryssa Thainá Mello Queiroz Cunha; Almira Oliveira Pereira; Roniery Correia Santos; Eduardo Zancopé; Sebastião  Alves Pinto; Valtuir Barbosa Félix; Rubens Jorge Silveira

doi:10.5327/2525-5711.326

Autores/as

Laryssa Thainá Mello Queiroz Cunha Department of oral diagnosis, Semiology and oral Pathology areas, Piracicaba Dental School, State University of Campinas (UNICAMP) https://orcid.org/0000-0003-1357-4129
Almira Oliveira Pereira Department of oral diagnosis, Semiology and oral Pathology areas, Piracicaba Dental School, State University of Campinas (UNICAMP)
Roniery Correia Santos Department of Psychology, IPOG - Instituto de Pós-Graduação e Graduação, Goiânia, Goiás, Brazil https://orcid.org/0000-0002-8481-1147
Eduardo Zancopé Department of Occlusion, Fixed Prosthesis and Dental Materials, School of Dentistry, Federal University of Uberlândia, Uberlândia, Minas Gerais, Brazil https://orcid.org/0000-0002-6567-4810
Sebastião Alves Pinto 5Pathologist, Goiano Institute of Oncology and Hematology, Goiânia, Goiás, Brazil
Valtuir Barbosa Félix Department of Oral Pathology, University Hospital of the Federal University of Alagoas, Maceió, Alagoas, Brasil https://orcid.org/0000-0002-2961-2487
Rubens Jorge Silveira Department of Oral and Maxillofacial Surgery and Traumatology, Pontifical Catholic University of Goiás (PUC - GOIÁS), https://orcid.org/0000-0002-3234-2158

DOI:

https://doi.org/10.5327/2525-5711.326

Palabras clave:

Cherubism, Facial deformities, Quality of life

Resumen

El querubismo es una osteodisplasia fibroósea poco frecuente que se caracteriza por la expansión simétrica de los maxilares, que suele producir deformidades faciales y deterioro funcional. Este estudio presenta el caso de un paciente pediátrico diagnosticado con querubismo que se sometió a una intervención quirúrgica temprana para mejorar la calidad de vida y reducir los impactos psicosociales asociados a la enfermedad. Se aplicó el cuestionario PedsQL™ 4.0 para evaluar la calidad de vida antes y después del procedimiento quirúrgico. Los resultados demostraron una mejora significativa en los dominios social y escolar, lo que refleja una reducción de la carga psicosocial del querubismo. Seis meses después del procedimiento, no se observaron complicaciones significativas ni signos de recurrencia, lo que destaca la eficacia de la intervención temprana. Estos hallazgos sugieren que un abordaje quirúrgico temprano es una estrategia valiosa para optimizar la calidad de vida y minimizar los efectos negativos del querubismo, en particular en niños en desarrollo social y académico.

Palabras clave: Querubismo; Deformidades faciales; Calidad de vida.

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